Stewart-Treves Syndrome: Associated Malignancy
Stewart-Treves syndrome is a rare complication characterized by the development of specific types of cancer.
Understanding Stewart-Treves Syndrome
This condition typically arises in patients with chronic lymphedema, most commonly seen after radiation therapy and mastectomy for breast cancer. The sustained swelling and inflammation create an environment conducive to malignant transformation.
Identifying the Malignancy
The primary malignancy associated with Stewart-Treves syndrome is:
- Lymphangiosarcoma: This is a type of soft tissue sarcoma originating from the lymphatic vessels. It is also often referred to as angiosarcoma in this context.
While other skin cancers like basal cell carcinoma or malignant melanoma can occur, they are not specifically linked to the pathogenesis of Stewart-Treves syndrome. Liposarcoma is a malignancy of fat tissue and is unrelated.
Therefore, the malignancy specifically associated with Stewart-Treves syndrome is Lymphangiosarcoma.
Important Questions from Lymphatic System
- An infant presented in the surgical OPD with complaints of a unilateral swelling in the neck. The swelling was soft, cystic, partially compressible and brilliantly transilluminant. The most probable diagnosis is
- A 52 year old female underwent MRM (Modified Radical Mastectomy). After few years, she developed lymphedema of the ipsilateral arm. Which of the following malignancy can develop in her arm?
- An infant presented in the surgical OPD with complaints of a unilateral swelling in the neck. The swelling was soft, cystic, partially compressible and brilliantly transilluminant. The most probable diagnosis is
- Which of the following statements regarding lymphoedema are correct?
1. Patients experience constant dull ache and even severe pain sometimes
2. Manual lymphatic drainage has a role
3. Primary lymphoedema is caused by congenital lymphatic dysplasia
4. Nonne Milroy's disease is a type of primary lymphoedema
Select the correct answer using the code given below: - In India, the commonest cause of unilateral lymphoedema of lower limb is:
